What Is Shone Syndrome?
Shone syndrome is a rare heart problem. It starts before birth. It blocks blood flow through the left side of the heart. It’s also called Shone’s complex.
It usually includes four issues:
- A tight mitral valve
- A bicuspid aortic valve (only two flaps instead of three)
- Aortic valve stenosis
- Coarctation of the aorta (a narrow spot in the aorta)
These issues stop blood from moving out of the heart the way it should. The heart works harder to pump blood. This is called left heart obstruction and it often requires effective blood pressure management to reduce strain on the heart.
What Causes It?
Shone syndrome is a congenital heart defect. That means it starts before birth. The heart does not form the right way. Doctors don’t always know why.
It may be tied to genes. Shone’s complex genetics is still being studied. Some babies are more at risk than others.
Symptoms
Signs can show up early or later in life. Many babies show signs in the first few months. Some people are not diagnosed until they are adults.
Common symptoms:
This condition can affect both infants and adults.
How It’s Found
Doctors often hear a murmur and order tests. These may include:
These tests show how the valves and aorta are working.
This is where BaleDoneen can help.
We help people with heart defects manage long-term risks. Our team offers tests, tracking, and simple plans that help prevent heart attack and protect your heart from early damage.
Treatment
Shone syndrome treatment depends on how blocked the heart is.
Some people need care right away. Others are watched over time.
Options include:
- Medicine to help the heart pump
- Surgery to open or replace tight valves
- Balloon procedures to widen the aorta
- Pediatric cardiac surgery for babies
- Regular follow-up with a heart doctor to monitor for heart failure or other complications
Most people need care more than once as they grow.
Life Expectancy
Shone’s syndrome life expectancy depends on how early it is found and how well it is treated. Many children live full lives with good care. Some will need lifelong checkups.